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AGGRESSIVE FIBROMATOSIS [1 record]
Record 1 - internal organization data 2006-01-12
Record 1, English
Record 1, Subject field(s)
- Cancers and Oncology
- Muscles and Tendons
Record 1, Main entry term, English
- desmoid tumor
1, record 1, English, desmoid%20tumor
correct
Record 1, Abbreviations, English
Record 1, Synonyms, English
- aggressive fibromatosis 1, record 1, English, aggressive%20fibromatosis
- desmoid 2, record 1, English, desmoid
Record 1, Textual support, English
Record number: 1, Textual support number: 1 CONT
Desmoid tumors often appear as infiltrative, usually well-differentiated, firm overgrowths of fibrous tissue, and they are locally aggressive. The synonym "aggressive fibromatosis" describes the marked cellularity and aggressive local behaviour. This course and the tendency for recurrence make the treatment of these relatively rare fibrous tumors challenging.... Although desmoid tumors most commonly arise from the rectus abdominis muscle in postpartum women and in scars due to abdominal surgery, they may arise in any skeletal muscle. The tumors tend to infiltrate adjacent muscle bundles, frequently entrapping them and causing their degeneration. 1, record 1, English, - desmoid%20tumor
Record 1, Key term(s)
- desmoid tumour
Record 1, French
Record 1, Domaine(s)
- Cancers et oncologie
- Muscles et tendons
Record 1, Main entry term, French
- tumeur desmoïde
1, record 1, French, tumeur%20desmo%C3%AFde
correct, feminine noun
Record 1, Abbreviations, French
Record 1, Synonyms, French
- fibromatose agressive 2, record 1, French, fibromatose%20agressive
feminine noun
Record 1, Textual support, French
Record number: 1, Textual support number: 1 CONT
La tumeur desmoïde afflige essentiellement la femme, surtout au cours d'une grossesse ou à sa suite. C'est une pseudotumeur fibrolastique qui se développe à la jonction musculo-aponévrique des muscles de la paroi abdominale, en particulier du grand droit. Elles est formée de fibroblastes matures sans atypie cellulaire. Elle dissocie les fibres musculaires striées qui s'atrophient et prennent un faux aspect de cellules géantes. Ce type de fibromatose s'observe aussi, quoique très rarement chez l'homme et chez l'enfant, dans les grosses masses musculaires de l'organisme. 3, record 1, French, - tumeur%20desmo%C3%AFde
Record number: 1, Textual support number: 1 OBS
Les tumeurs desmoïdes ou fibromatoses agressives sont des proliférations fibreuses infiltrantes, récidivantes mais non métastasiantes [...] Elles sont localisées soit dans les aponévroses des muscles périphériques (45 %), soit dans les muscles de la paroi abdominale (45 %) soit plus rarement dans les régions mésentériques ou rétropéritonéales (10 %). 2, record 1, French, - tumeur%20desmo%C3%AFde
Record 1, Spanish
Record 1, Textual support, Spanish
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