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Consult the Government of Canada’s terminology data bank.
HEMOPHILIA [27 records]
Record 1 - internal organization data 2017-09-22
Record 1, English
Record 1, Subject field(s)
- National Bodies and Committees (Canadian)
- Blood
Record 1, Main entry term, English
- Canadian Hemophilia Society
1, record 1, English, Canadian%20Hemophilia%20Society
correct
Record 1, Abbreviations, English
- CHS 2, record 1, English, CHS
correct
Record 1, Synonyms, English
Record 1, Textual support, English
Record number: 1, Textual support number: 1 OBS
The Canadian Hemophilia Society is committed to improving the health and quality of life of all people in Canada with inherited bleeding disorders and ultimately finding cures. 3, record 1, English, - Canadian%20Hemophilia%20Society
Record 1, French
Record 1, Domaine(s)
- Organismes et comités nationaux canadiens
- Sang
Record 1, Main entry term, French
- Société canadienne de l'hémophilie
1, record 1, French, Soci%C3%A9t%C3%A9%20canadienne%20de%20l%27h%C3%A9mophilie
correct, feminine noun
Record 1, Abbreviations, French
- SCH 2, record 1, French, SCH
correct, feminine noun
Record 1, Synonyms, French
Record 1, Textual support, French
Record number: 1, Textual support number: 1 OBS
La Société canadienne de l'hémophilie est déterminée à améliorer l'état de santé et la qualité de vie de toutes les personnes atteintes de troubles héréditaires de la coagulation au Canada et, ultimement, à trouver des remèdes définitifs. 2, record 1, French, - Soci%C3%A9t%C3%A9%20canadienne%20de%20l%27h%C3%A9mophilie
Record 1, Spanish
Record 1, Textual support, Spanish
Record 2 - internal organization data 2011-11-22
Record 2, English
Record 2, Subject field(s)
- Non-Gov. Provincial Bodies and Committees (Canadian)
- Blood
Record 2, Main entry term, English
- Hemophilia Ontario
1, record 2, English, Hemophilia%20Ontario
correct
Record 2, Abbreviations, English
Record 2, Synonyms, English
Record 2, Textual support, English
Record number: 2, Textual support number: 1 OBS
Founded in 1956, Hemophilia Ontario is the Ontario Chapter of the Canadian Hemophilia Society.... Hemophilia Ontario is committed to improving the health, and quality of life for all people with a bleeding disorder, and to find a cure. 1, record 2, English, - Hemophilia%20Ontario
Record 2, French
Record 2, Domaine(s)
- Organismes et comités provinciaux non gouv. canadiens
- Sang
Record 2, Main entry term, French
- Hémophilie Ontario
1, record 2, French, H%C3%A9mophilie%20Ontario
correct
Record 2, Abbreviations, French
Record 2, Synonyms, French
Record 2, Textual support, French
Record number: 2, Textual support number: 1 OBS
Section de la Société canadienne de l'hémophilie. 1, record 2, French, - H%C3%A9mophilie%20Ontario
Record 2, Spanish
Record 2, Textual support, Spanish
Record 3 - internal organization data 2011-10-31
Record 3, English
Record 3, Subject field(s)
- Titles of Documents and Works
Record 3, Main entry term, English
- A Hands-on Guide to Planning and Evaluation - How to Plan and Evaluate Programs in Community Organizations 1, record 3, English, A%20Hands%2Don%20Guide%20to%20Planning%20and%20Evaluation%20%2D%20How%20to%20Plan%20and%20Evaluate%20Programs%20in%20Community%20Organizations
Record 3, Abbreviations, English
Record 3, Synonyms, English
- A Hands-On Guide to Planning and Evaluation: How to Plan and Evaluate Programs in Community-Based Organization 2, record 3, English, A%20Hands%2DOn%20Guide%20to%20Planning%20and%20Evaluation%3A%20How%20to%20Plan%20and%20Evaluate%20Programs%20in%20Community%2DBased%20Organization
Record 3, Textual support, English
Record number: 3, Textual support number: 1 OBS
Canadian Hemophilia Association(1994). 2, record 3, English, - A%20Hands%2Don%20Guide%20to%20Planning%20and%20Evaluation%20%2D%20How%20to%20Plan%20and%20Evaluate%20Programs%20in%20Community%20Organizations
Record 3, Key term(s)
- A Hands-On Guide to Planning and Evaluation
Record 3, French
Record 3, Domaine(s)
- Titres de documents et d'œuvres
Record 3, Main entry term, French
- Guide pratique de planification et d'évaluation - Comment planifier et évaluer les programmes dans des organismes communautaires 1, record 3, French, Guide%20pratique%20de%20planification%20et%20d%27%C3%A9valuation%20%2D%20Comment%20planifier%20et%20%C3%A9valuer%20les%20programmes%20dans%20des%20organismes%20communautaires
Record 3, Abbreviations, French
Record 3, Synonyms, French
Record 3, Textual support, French
Record number: 3, Textual support number: 1 OBS
Programme d'action communautaire sur le sida, Santé Canada. 2, record 3, French, - Guide%20pratique%20de%20planification%20et%20d%27%C3%A9valuation%20%2D%20Comment%20planifier%20et%20%C3%A9valuer%20les%20programmes%20dans%20des%20organismes%20communautaires
Record number: 3, Textual support number: 2 OBS
Société canadienne de l'hémophilie (1994). 3, record 3, French, - Guide%20pratique%20de%20planification%20et%20d%27%C3%A9valuation%20%2D%20Comment%20planifier%20et%20%C3%A9valuer%20les%20programmes%20dans%20des%20organismes%20communautaires
Record 3, Key term(s)
- Guide pratique de planification et d'évaluation
- Guide pratique de planification et d'évaluation : comment planifier et évaluer les programmes dans des organismes communautaires
Record 3, Spanish
Record 3, Textual support, Spanish
Record 4 - internal organization data 2011-08-16
Record 4, English
Record 4, Subject field(s)
- Symptoms (Medicine)
- Musculoskeletal System
Record 4, Main entry term, English
- hemorrhagic diathesis
1, record 4, English, hemorrhagic%20diathesis
correct
Record 4, Abbreviations, English
Record 4, Synonyms, English
Record 4, Textual support, English
Record number: 4, Textual support number: 1 DEF
Any tendency to spontaneous bleeding or bleeding from trivial trauma caused by a defect in clotting or a flaw in the structure of blood vessels, as in hemophilia, purpura, scurvy, or vitamin K deficiency. 2, record 4, English, - hemorrhagic%20diathesis
Record number: 4, Textual support number: 1 OBS
Can be seen in primary amyloidosis or be secondary to anti-inflammatory drugs. 3, record 4, English, - hemorrhagic%20diathesis
Record 4, French
Record 4, Domaine(s)
- Symptômes (Médecine)
- Appareil locomoteur (Médecine)
Record 4, Main entry term, French
- diathèse hémorragique
1, record 4, French, diath%C3%A8se%20h%C3%A9morragique
correct, feminine noun
Record 4, Abbreviations, French
Record 4, Synonyms, French
Record 4, Textual support, French
Record number: 4, Textual support number: 1 DEF
Syndrome hémorragique dû à une anomalie du système vasculaire, plaquettaire ou plasmatique. 2, record 4, French, - diath%C3%A8se%20h%C3%A9morragique
Record number: 4, Textual support number: 1 OBS
Peut s'observer dans l'amylose primitive ou être due à l'ingestion d'anti-inflammatoires. 3, record 4, French, - diath%C3%A8se%20h%C3%A9morragique
Record 4, Spanish
Record 4, Campo(s) temático(s)
- Síntomas (Medicina)
- Sistema musculoesquelético (Medicina)
Record 4, Main entry term, Spanish
- diátesis hemorrágica
1, record 4, Spanish, di%C3%A1tesis%20hemorr%C3%A1gica
correct, feminine noun
Record 4, Abbreviations, Spanish
Record 4, Synonyms, Spanish
Record 4, Textual support, Spanish
Record 5 - internal organization data 2011-08-12
Record 5, English
Record 5, Subject field(s)
- Blood
Record 5, Main entry term, English
- hemophilia A
1, record 5, English, hemophilia%20A
correct
Record 5, Abbreviations, English
Record 5, Synonyms, English
Record 5, Textual support, English
Record number: 5, Textual support number: 1 OBS
Term(s) taken from a Canadian laboratory-equipment company’s catalogue. 1, record 5, English, - hemophilia%20A
Record 5, French
Record 5, Domaine(s)
- Sang
Record 5, Main entry term, French
- hémophilie A
1, record 5, French, h%C3%A9mophilie%20A
feminine noun
Record 5, Abbreviations, French
Record 5, Synonyms, French
Record 5, Textual support, French
Record number: 5, Textual support number: 1 OBS
Terme(s) tiré(s) du catalogue d'une compagnie canadienne d'équipement de laboratoire. 1, record 5, French, - h%C3%A9mophilie%20A
Record 5, Spanish
Record 5, Textual support, Spanish
Record 6 - internal organization data 2011-02-23
Record 6, English
Record 6, Subject field(s)
- Medical and Hospital Organization
- General Medicine, Hygiene and Health
- Health Insurance
Record 6, Main entry term, English
- comprehensive care
1, record 6, English, comprehensive%20care
correct
Record 6, Abbreviations, English
Record 6, Synonyms, English
- comprehensive health care 2, record 6, English, comprehensive%20health%20care
correct
- comprehensive medical care 3, record 6, English, comprehensive%20medical%20care
correct
Record 6, Textual support, English
Record number: 6, Textual support number: 1 CONT
The [center] provides comprehensive care for persons with hemophilia, von Willebrands disease, and other coagulation disorders. Comprehensive care means that the person, not just the condition, is the focus of concern. A major objective of comprehensive care is providing support and evaluation of the medical and social factors affecting the individual and family. Early and ongoing intervention helps prevent the occurrence of complications. The multidisciplinary team... offers evaluation, counseling, education and advocacy to help the individual realize full life potential. The comprehensive care team includes : the individual and family, the hematologist, the nurse coordinator, the social worker, the physical therapist and the orthopedic physician, the dentist. and the geneticist. 4, record 6, English, - comprehensive%20care
Record 6, French
Record 6, Domaine(s)
- Organisation médico-hospitalière
- Médecine générale, hygiène et santé
- Assurance-maladie
Record 6, Main entry term, French
- soins de santé intégrés
1, record 6, French, soins%20de%20sant%C3%A9%20int%C3%A9gr%C3%A9s
correct, masculine noun, plural
Record 6, Abbreviations, French
Record 6, Synonyms, French
- soins intégrés 2, record 6, French, soins%20int%C3%A9gr%C3%A9s
correct, masculine noun, plural
- soins de santé complets 3, record 6, French, soins%20de%20sant%C3%A9%20complets
correct, masculine noun, plural
- soins complets 4, record 6, French, soins%20complets
correct, masculine noun, plural
- soins de santé globaux 5, record 6, French, soins%20de%20sant%C3%A9%20globaux
correct, masculine noun, plural
- soins globaux 6, record 6, French, soins%20globaux
correct, masculine noun, plural
Record 6, Textual support, French
Record number: 6, Textual support number: 1 DEF
Soins de santé et d'aide sociale coordonnés et adaptés aux besoins de chaque [personne selon] une approche considérée comme un moyen efficace de fournir des mesures préventives. 7, record 6, French, - soins%20de%20sant%C3%A9%20int%C3%A9gr%C3%A9s
Record number: 6, Textual support number: 1 CONT
Un modèle de soins proposé pour un meilleur suivi des maladies chroniques est celui des soins intégrés[,qui] fait appel à des équipes multidisciplinaires et comporte des interventions portant sur l'organisation des soins, sur le système des soins, ainsi que sur la prise en charge par le patient lui-même de sa maladie [...] Le traitement des affections chroniques passe également par une modification du comportement quotidien et de l'hygiène de vie. [...] Un axe prioritaire est celui de la médecine préventive [...] 8, record 6, French, - soins%20de%20sant%C3%A9%20int%C3%A9gr%C3%A9s
Record number: 6, Textual support number: 2 CONT
Soins globaux signifie qu'une équipe pluridisciplinaire accompagne le malade: les médecins (dont les médecins traitants), les infirmiers, des kinésithérapeutes, mais aussi des assistants sociaux, des psychologues, des conseillers philosophiques et religieux. 6, record 6, French, - soins%20de%20sant%C3%A9%20int%C3%A9gr%C3%A9s
Record 6, Spanish
Record 6, Campo(s) temático(s)
- Organización médica y hospitalaria
- Medicina, Higiene y Salud
- Seguro médico
Record 6, Main entry term, Spanish
- atención integral de salud
1, record 6, Spanish, atenci%C3%B3n%20integral%20de%20salud
feminine noun
Record 6, Abbreviations, Spanish
Record 6, Synonyms, Spanish
- cuidado integral de la salud 2, record 6, Spanish, cuidado%20integral%20de%20la%20salud
masculine noun
Record 6, Textual support, Spanish
Record 7 - internal organization data 2011-01-05
Record 7, English
Record 7, Subject field(s)
- Blood
Record 7, Main entry term, English
- hemophilia B
1, record 7, English, hemophilia%20B
correct
Record 7, Abbreviations, English
Record 7, Synonyms, English
- Christmas disease 2, record 7, English, Christmas%20disease
correct
- factor 1X deficiency 3, record 7, English, factor%201X%20deficiency
correct
Record 7, Textual support, English
Record number: 7, Textual support number: 1 DEF
An X-linked hereditary bleeding disease caused by a deficiency of factor 1X. 3, record 7, English, - hemophilia%20B
Record 7, French
Record 7, Domaine(s)
- Sang
Record 7, Main entry term, French
- hémophilie B
1, record 7, French, h%C3%A9mophilie%20B
correct, feminine noun
Record 7, Abbreviations, French
Record 7, Synonyms, French
- déficit en facteur IX 2, record 7, French, d%C3%A9ficit%20en%20facteur%20IX
correct, masculine noun
- maladie de Christmas 3, record 7, French, maladie%20de%20Christmas
correct, feminine noun
Record 7, Textual support, French
Record number: 7, Textual support number: 1 DEF
Affection hémorragique liée au sexe et due à un déficit congénital en facteur antihémophilique B (facteur 1X). 4, record 7, French, - h%C3%A9mophilie%20B
Record number: 7, Textual support number: 1 CONT
La maladie de Christmas, du nom de Steven Christmas, un Canadien, qui, en 1952, a été le premier homme à recevoir un diagnostic de ce type distinct d'hémophilie et hémophilie par déficit en facteur IX, parce que c'est le facteur 9 (écrit en chiffres romains, IX), qui est la protéine sanguine déficitaire et dont l'absence ralentit le processus normal de coagulation. 3, record 7, French, - h%C3%A9mophilie%20B
Record 7, Spanish
Record 7, Textual support, Spanish
Record 8 - internal organization data 2010-02-05
Record 8, English
Record 8, Subject field(s)
- Bacterial Diseases
Record 8, Main entry term, English
- allergic disorder 1, record 8, English, allergic%20disorder
Record 8, Abbreviations, English
Record 8, Synonyms, English
Record 8, Textual support, English
Record number: 8, Textual support number: 1 OBS
E. examples of the hereditary diseases are hemophilia [certain nervous and mental diseases ] and a tendency to--, such as infantile eczema and bronchial asthma. 1, record 8, English, - allergic%20disorder
Record 8, French
Record 8, Domaine(s)
- Maladies bactériennes
Record 8, Main entry term, French
- affection allergique 1, record 8, French, affection%20allergique
Record 8, Abbreviations, French
Record 8, Synonyms, French
Record 8, Textual support, French
Record number: 8, Textual support number: 1 OBS
E.même dans les --, l'évolution spontanée des redoutables infirmités que sont l'asthme, l'eczéma (...) se fait (...) vers une atténuation des symptômes chez l'enfant grandissant. 1, record 8, French, - affection%20allergique
Record 8, Spanish
Record 8, Textual support, Spanish
Record 9 - internal organization data 2010-02-04
Record 9, English
Record 9, Subject field(s)
- Organizations, Administrative Units and Committees
- Lymphatic System
Record 9, Main entry term, English
- Canadian Hemophilia Clinic Directors Group 1, record 9, English, Canadian%20Hemophilia%20Clinic%20Directors%20Group
Record 9, Abbreviations, English
Record 9, Synonyms, English
Record 9, Textual support, English
Record number: 9, Textual support number: 1 OBS
Source : Letter from the Chairman of the Canadian Hemophilia Clinic Directors Group. 1, record 9, English, - Canadian%20Hemophilia%20Clinic%20Directors%20Group
Record 9, French
Record 9, Domaine(s)
- Organismes, unités administratives et comités
- Système lymphatique
Record 9, Main entry term, French
- Groupe des directeurs de cliniques canadiennes de traitement de l'hémophilie
1, record 9, French, Groupe%20des%20directeurs%20de%20cliniques%20canadiennes%20de%20traitement%20de%20l%27h%C3%A9mophilie
masculine noun
Record 9, Abbreviations, French
- GDCCTH 1, record 9, French, GDCCTH
masculine noun
Record 9, Synonyms, French
Record 9, Textual support, French
Record number: 9, Textual support number: 1 OBS
Source : Commission Krever. 1, record 9, French, - Groupe%20des%20directeurs%20de%20cliniques%20canadiennes%20de%20traitement%20de%20l%27h%C3%A9mophilie
Record 9, Spanish
Record 9, Textual support, Spanish
Record 10 - internal organization data 2008-01-29
Record 10, English
Record 10, Subject field(s)
- National Bodies and Committees (Canadian)
- Health Institutions
- Human Diseases - Various
- Blood
Record 10, Main entry term, English
- Association of Hemophilia Clinic Directors of Canada
1, record 10, English, Association%20of%20Hemophilia%20Clinic%20Directors%20of%20Canada
correct
Record 10, Abbreviations, English
- AHCDC 1, record 10, English, AHCDC
correct
Record 10, Synonyms, English
Record 10, Textual support, English
Record number: 10, Textual support number: 1 OBS
The goal of the AHCDC is to ensure excellent care for persons with congenital bleeding disorders in Canada through clinical services, research and education. 1, record 10, English, - Association%20of%20Hemophilia%20Clinic%20Directors%20of%20Canada
Record 10, French
Record 10, Domaine(s)
- Organismes et comités nationaux canadiens
- Établissements de santé
- Maladies humaines diverses
- Sang
Record 10, Main entry term, French
- L'Association Canadienne des Directeurs des Cliniques d'Hémophilie
1, record 10, French, L%27Association%20Canadienne%20des%20Directeurs%20des%20Cliniques%20d%27H%C3%A9mophilie
correct, feminine noun
Record 10, Abbreviations, French
Record 10, Synonyms, French
Record 10, Textual support, French
Record number: 10, Textual support number: 1 OBS
L'objectif de l'AHCDC est d'assurer aux personnes atteintes de coagulopathies héréditaires le meilleur traitement possible en offrant des soins d'excellence et en développant la recherche et l'enseignement. 1, record 10, French, - L%27Association%20Canadienne%20des%20Directeurs%20des%20Cliniques%20d%27H%C3%A9mophilie
Record 10, Spanish
Record 10, Textual support, Spanish
Record 11 - internal organization data 2005-04-11
Record 11, English
Record 11, Subject field(s)
- Blood
Record 11, Main entry term, English
- factor VIII
1, record 11, English, factor%20VIII
correct
Record 11, Abbreviations, English
Record 11, Synonyms, English
Record 11, Textual support, English
Record number: 11, Textual support number: 1 OBS
Coagulation factors are numerous proteins that circulate in the blood and transform from inactive to active forms whenever blood clotting is required.... The best known of the inherited disorders of coagulation are hemophilia A and B, associated with a decrease in the activity of Factor VIII or IX, respectively. 1, record 11, English, - factor%20VIII
Record 11, French
Record 11, Domaine(s)
- Sang
Record 11, Main entry term, French
- facteur VIII
1, record 11, French, facteur%20VIII
correct, masculine noun
Record 11, Abbreviations, French
Record 11, Synonyms, French
Record 11, Textual support, French
Record number: 11, Textual support number: 1 DEF
Molécule complexe (et volumineuse), faite d'une partie synthétisée par les cellules hépatiques (VIII : C) qui a une activité coagulante, et d'une partie synthétisée au niveau de la paroi interne des vaisseaux sanguins (VIII : WF ou facteur de Wildebrand). 2, record 11, French, - facteur%20VIII
Record 11, Spanish
Record 11, Campo(s) temático(s)
- Sangre
Record 11, Main entry term, Spanish
- factor VIII
1, record 11, Spanish, factor%20VIII
correct, masculine noun
Record 11, Abbreviations, Spanish
Record 11, Synonyms, Spanish
Record 11, Textual support, Spanish
Record number: 11, Textual support number: 1 DEF
Componente normal de la sangre que participa en la coagulación; en las personas hemofílicas no se produce por factores hereditarios. 1, record 11, Spanish, - factor%20VIII
Record 12 - internal organization data 2004-12-03
Record 12, English
Record 12, Subject field(s)
- Blood
Record 12, Main entry term, English
- hemophilia
1, record 12, English, hemophilia
correct
Record 12, Abbreviations, English
Record 12, Synonyms, English
Record 12, Textual support, English
Record number: 12, Textual support number: 1 DEF
A hereditary hemorrhagic diathesis characterized by haemarthrosis and deep tissue bleeding, due to deficient generation of intrinsic thromboplastin. 2, record 12, English, - hemophilia
Record 12, Key term(s)
- haemophilia
Record 12, French
Record 12, Domaine(s)
- Sang
Record 12, Main entry term, French
- hémophilie
1, record 12, French, h%C3%A9mophilie
correct, feminine noun
Record 12, Abbreviations, French
Record 12, Synonyms, French
Record 12, Textual support, French
Record number: 12, Textual support number: 1 DEF
Maladie génétique et héréditaire de la coagulation caractérisée par une propension aux hémorragies. 2, record 12, French, - h%C3%A9mophilie
Record 12, Spanish
Record 12, Campo(s) temático(s)
- Sangre
Record 12, Main entry term, Spanish
- hemofilia
1, record 12, Spanish, hemofilia
correct, feminine noun
Record 12, Abbreviations, Spanish
Record 12, Synonyms, Spanish
Record 12, Textual support, Spanish
Record number: 12, Textual support number: 1 DEF
Padecimiento hereditario caracterizado por una coagulación inadecuada, por ausencia de los factores VIII ó IX en la sangre. 2, record 12, Spanish, - hemofilia
Record 13 - internal organization data 2004-04-16
Record 13, English
Record 13, Subject field(s)
- Titles of Films
- Dietetics
- Hygiene and Health
Record 13, Main entry term, English
- Healthy Eating Makes a Difference
1, record 13, English, Healthy%20Eating%20Makes%20a%20Difference
correct
Record 13, Abbreviations, English
Record 13, Synonyms, English
Record 13, Textual support, English
Record number: 13, Textual support number: 1 OBS
National Film Board of Canada. Produced by Savoury Productions with the financial assistance of the Canadian Hemophilia Society and Health and Welfare Canada. 1, record 13, English, - Healthy%20Eating%20Makes%20a%20Difference
Record 13, French
Record 13, Domaine(s)
- Titres de films
- Diététique
- Hygiène et santé
Record 13, Main entry term, French
- Être mieux en mangeant mieux
1, record 13, French, %C3%8Atre%20mieux%20en%20mangeant%20mieux
correct
Record 13, Abbreviations, French
Record 13, Synonyms, French
Record 13, Textual support, French
Record 13, Spanish
Record 13, Textual support, Spanish
Record 14 - internal organization data 2004-03-23
Record 14, English
Record 14, Subject field(s)
- International Bodies and Committees
- Blood
Record 14, Main entry term, English
- World Federation of Hemophilia
1, record 14, English, World%20Federation%20of%20Hemophilia
correct
Record 14, Abbreviations, English
- WFH 2, record 14, English, WFH
correct
Record 14, Synonyms, English
Record 14, Textual support, English
Record number: 14, Textual support number: 1 OBS
The canadian office is established in Montréal, Quebec. 3, record 14, English, - World%20Federation%20of%20Hemophilia
Record 14, French
Record 14, Domaine(s)
- Organismes et comités internationaux
- Sang
Record 14, Main entry term, French
- Fédération mondiale de l'hémophilie
1, record 14, French, F%C3%A9d%C3%A9ration%20mondiale%20de%20l%27h%C3%A9mophilie
correct, feminine noun
Record 14, Abbreviations, French
- FMH 1, record 14, French, FMH
correct, feminine noun
Record 14, Synonyms, French
Record 14, Textual support, French
Record number: 14, Textual support number: 1 OBS
Au Canada, l'organisme est établi à Montréal (Québec). 2, record 14, French, - F%C3%A9d%C3%A9ration%20mondiale%20de%20l%27h%C3%A9mophilie
Record 14, Spanish
Record 14, Textual support, Spanish
Record 15 - internal organization data 2004-02-06
Record 15, English
Record 15, Subject field(s)
- Names of Special Years, Weeks, Days
- Blood
Record 15, Main entry term, English
- World Hemophilia Day
1, record 15, English, World%20Hemophilia%20Day
correct
Record 15, Abbreviations, English
Record 15, Synonyms, English
Record 15, Textual support, English
Record number: 15, Textual support number: 1 OBS
April 17, World Hemophilia Day, is celebrated by hemophilia organizations around the world, and provides an opportunity to increase awareness of hemophilia. World Hemophilia Day is a unique opportunity to raise public awareness of hemophilia and to bring attention to the tremendous need for improved diagnosis and treatment. The WFH(World Federation of Hemophilia) encourages all hemophilia organizations to plan activities for World Hemophilia Day to help raise awareness and support among the general public. 1, record 15, English, - World%20Hemophilia%20Day
Record 15, French
Record 15, Domaine(s)
- Désignations d'années, de semaines et de jours spéciaux
- Sang
Record 15, Main entry term, French
- Journée mondiale de l'hémophilie
1, record 15, French, Journ%C3%A9e%20mondiale%20de%20l%27h%C3%A9mophilie
correct, feminine noun
Record 15, Abbreviations, French
Record 15, Synonyms, French
Record 15, Textual support, French
Record number: 15, Textual support number: 1 OBS
Le 17 avril, des organisations de l'hémophilie partout dans le monde célèbrent la Journée mondiale de l'hémophilie et profitent de l'occasion pour mieux faire connaître l'hémophilie. La Journée mondiale de l'hémophilie est une occasion unique de mieux faire connaître l'hémophilie et d'attirer l'attention sur le besoin énorme d'étendre le diagnostic et le traitement. La FMH (Fédération mondiale de l'hémophilie) invite toutes les organisations de l'hémophilie à planifier des activités pour la Journée, afin de sensibiliser le public et de rallier son soutien. 1, record 15, French, - Journ%C3%A9e%20mondiale%20de%20l%27h%C3%A9mophilie
Record 15, Spanish
Record 15, Textual support, Spanish
Record 16 - internal organization data 2003-11-14
Record 16, English
Record 16, Subject field(s)
- Blood
Record 16, Main entry term, English
- factor XII
1, record 16, English, factor%20XII
correct
Record 16, Abbreviations, English
Record 16, Synonyms, English
- Hageman factor 1, record 16, English, Hageman%20factor
correct
- HF 2, record 16, English, HF
correct
- HF 2, record 16, English, HF
Record 16, Textual support, English
Record number: 16, Textual support number: 1 DEF
A factor that initiates blood clotting and one that is deficient in hemophilia. 2, record 16, English, - factor%20XII
Record 16, Key term(s)
- factor 12
Record 16, French
Record 16, Domaine(s)
- Sang
Record 16, Main entry term, French
- facteur XII
1, record 16, French, facteur%20XII
correct, masculine noun
Record 16, Abbreviations, French
Record 16, Synonyms, French
- facteur Hageman 2, record 16, French, facteur%20Hageman
correct, masculine noun
Record 16, Textual support, French
Record number: 16, Textual support number: 1 CONT
Les facteurs de la coagulation. [Le] facteur XII ou facteur Hageman augmente la perméabilité capillaire, 1, record 16, French, - facteur%20XII
Record 16, Key term(s)
- facteur 12
Record 16, Spanish
Record 16, Campo(s) temático(s)
- Sangre
Record 16, Main entry term, Spanish
- factor Hageman
1, record 16, Spanish, factor%20Hageman
correct, masculine noun
Record 16, Abbreviations, Spanish
Record 16, Synonyms, Spanish
Record 16, Textual support, Spanish
Record number: 16, Textual support number: 1 DEF
Proteína plasmática de los mamíferos, que interviene en la mecanismo de la coagulación sanguínea, activando la precalicreína. 1, record 16, Spanish, - factor%20Hageman
Record 17 - internal organization data 2003-10-27
Record 17, English
Record 17, Subject field(s)
- National Bodies and Committees (Canadian)
- Blood
Record 17, Main entry term, English
- Canadian Association of Nurses in Hemophilia Care
1, record 17, English, Canadian%20Association%20of%20Nurses%20in%20Hemophilia%20Care
correct
Record 17, Abbreviations, English
- CANHC 2, record 17, English, CANHC
correct
Record 17, Synonyms, English
Record 17, French
Record 17, Domaine(s)
- Organismes et comités nationaux canadiens
- Sang
Record 17, Main entry term, French
- Association Canadienne des Infirmières et Infirmiers en Hémophilie
1, record 17, French, Association%20Canadienne%20des%20Infirmi%C3%A8res%20et%20Infirmiers%20en%20H%C3%A9mophilie
correct, feminine noun
Record 17, Abbreviations, French
Record 17, Synonyms, French
Record 17, Textual support, French
Record 17, Spanish
Record 17, Textual support, Spanish
Record 18 - internal organization data 2003-05-09
Record 18, English
Record 18, Subject field(s)
- Blood
- Biotechnology
Record 18, Main entry term, English
- factor IX
1, record 18, English, factor%20IX
correct
Record 18, Abbreviations, English
Record 18, Synonyms, English
- autoprothrombin II 1, record 18, English, autoprothrombin%20II
correct
- Christmas factor 2, record 18, English, Christmas%20factor
correct
- antihemophilic factor B 1, record 18, English, antihemophilic%20factor%20B
correct
- plasma thromboplastin component 1, record 18, English, plasma%20thromboplastin%20component
correct
- PTC 1, record 18, English, PTC
correct
- PTC 1, record 18, English, PTC
Record 18, Textual support, English
Record number: 18, Textual support number: 1 DEF
A relatively storage-stable substance involved in the intrinsic pathway of blood coagulation; upon activation, it activates factor X. 3, record 18, English, - factor%20IX
Record number: 18, Textual support number: 1 OBS
Deficiency results in a hemorrhagic syndrome called hemophilia B, resembling hemophilia A. 3, record 18, English, - factor%20IX
Record 18, Key term(s)
- F-IX
- FIX
- F IX
- factor 9
- F9
- antihemophilic B factor
Record 18, French
Record 18, Domaine(s)
- Sang
- Biotechnologie
Record 18, Main entry term, French
- facteur IX
1, record 18, French, facteur%20IX
correct, masculine noun
Record 18, Abbreviations, French
- FIX 2, record 18, French, FIX
correct, masculine noun
Record 18, Synonyms, French
- facteur antihémophilique B 3, record 18, French, facteur%20antih%C3%A9mophilique%20B
correct, masculine noun
- facteur antihémolytique B 4, record 18, French, facteur%20antih%C3%A9molytique%20B
masculine noun
Record 18, Textual support, French
Record number: 18, Textual support number: 1 DEF
[L'une des] substances chimiques présentes dans le plasma qui après avoir été activées contrôlent de façon spécifique une série de réactions en cascade qui sont à l'origine du mécanisme complexe de la coagulation. 4, record 18, French, - facteur%20IX
Record number: 18, Textual support number: 1 CONT
Les protéines qui manquent aux hémophiles sont appelées facteur VIII et facteur IX. Dans le premier cas, on parle d'hémophilie A, représentant environ 85 % des cas. Dans le second d'hémophilie B, affectant 15 % de la population hémophile. 5, record 18, French, - facteur%20IX
Record 18, Key term(s)
- F-IX
- F IX
- facteur 9
- F9
- facteur christmas
Record 18, Spanish
Record 18, Campo(s) temático(s)
- Sangre
- Biotecnología
Record 18, Main entry term, Spanish
- factor Christmas
1, record 18, Spanish, factor%20Christmas
correct, masculine noun
Record 18, Abbreviations, Spanish
Record 18, Synonyms, Spanish
- factor de Christmas 2, record 18, Spanish, factor%20de%20Christmas
masculine noun
Record 18, Textual support, Spanish
Record 19 - internal organization data 2001-07-31
Record 19, English
Record 19, Subject field(s)
- Blood
Record 19, Main entry term, English
- hemophiliac
1, record 19, English, hemophiliac
correct, noun
Record 19, Abbreviations, English
Record 19, Synonyms, English
Record 19, Textual support, English
Record number: 19, Textual support number: 1 DEF
An individual exhibiting hemophilia. 1, record 19, English, - hemophiliac
Record 19, French
Record 19, Domaine(s)
- Sang
Record 19, Main entry term, French
- hémophile
1, record 19, French, h%C3%A9mophile
correct, masculine and feminine noun
Record 19, Abbreviations, French
Record 19, Synonyms, French
Record 19, Textual support, French
Record number: 19, Textual support number: 1 DEF
Personne atteinte d'hémophilie. 2, record 19, French, - h%C3%A9mophile
Record 19, Spanish
Record 19, Textual support, Spanish
Record 20 - internal organization data 2001-03-13
Record 20, English
Record 20, Subject field(s)
- Titles of Monographs
- Blood
Record 20, Main entry term, English
- Hemophilia Today
1, record 20, English, Hemophilia%20Today
correct, Canada
Record 20, Abbreviations, English
Record 20, Synonyms, English
Record 20, Textual support, English
Record number: 20, Textual support number: 1 OBS
Canadian Hemophilia Society. 1, record 20, English, - Hemophilia%20Today
Record 20, French
Record 20, Domaine(s)
- Titres de monographies
- Sang
Record 20, Main entry term, French
- L'hémophilie de nos jours
1, record 20, French, L%27h%C3%A9mophilie%20de%20nos%20jours
correct, feminine noun, Canada
Record 20, Abbreviations, French
Record 20, Synonyms, French
Record 20, Textual support, French
Record number: 20, Textual support number: 1 OBS
Société canadienne de l'hémophilie. 1, record 20, French, - L%27h%C3%A9mophilie%20de%20nos%20jours
Record 20, Spanish
Record 20, Textual support, Spanish
Record 21 - internal organization data 2000-03-23
Record 21, English
Record 21, Subject field(s)
- Blood
- Injections, Tubing and Transfusions (Medicine)
Record 21, Main entry term, English
- factor replacement therapy 1, record 21, English, factor%20replacement%20therapy
Record 21, Abbreviations, English
Record 21, Synonyms, English
Record 21, Textual support, English
Record number: 21, Textual support number: 1 CONT
The basic treatment to stop or prevent bleeding in people with hemophilia A and B is factor replacement therapy. This is the infusion(injection into the bloodstream) of Factor VIII and IX concentrates to prevent or control bleeding. 1, record 21, English, - factor%20replacement%20therapy
Record 21, French
Record 21, Domaine(s)
- Sang
- Injections, tubages et transfusions (Médecine)
Record 21, Main entry term, French
- thérapie par facteurs de remplacement
1, record 21, French, th%C3%A9rapie%20par%20facteurs%20de%20remplacement
feminine noun
Record 21, Abbreviations, French
Record 21, Synonyms, French
Record 21, Textual support, French
Record number: 21, Textual support number: 1 CONT
Le traitement de base qui permet d'enrayer ou de prévenir les saignements chez les personnes atteintes d'hémophilie A et B est le traitement par facteur de remplacement. Il s'agit d'une perfusion (injection dans la circulation sanguine) de concentré de facteur VIII ou IX administrée pour empêcher ou maîtriser l'hémorragie. 1, record 21, French, - th%C3%A9rapie%20par%20facteurs%20de%20remplacement
Record 21, Spanish
Record 21, Textual support, Spanish
Record 22 - internal organization data 2000-02-02
Record 22, English
Record 22, Subject field(s)
- Organizations, Administrative Units and Committees
- Health Institutions
- Blood
Record 22, Main entry term, English
- Hemophilia Clinic 1, record 22, English, Hemophilia%20Clinic
Record 22, Abbreviations, English
Record 22, Synonyms, English
Record 22, Textual support, English
Record number: 22, Textual support number: 1 OBS
Source(s): Children’s Hospital Lexicon 1999. 1, record 22, English, - Hemophilia%20Clinic
Record 22, French
Record 22, Domaine(s)
- Organismes, unités administratives et comités
- Établissements de santé
- Sang
Record 22, Main entry term, French
- Clinique d'hémophilie
1, record 22, French, Clinique%20d%27h%C3%A9mophilie
feminine noun
Record 22, Abbreviations, French
Record 22, Synonyms, French
Record 22, Textual support, French
Record number: 22, Textual support number: 1 OBS
Source(s) : Lexique 1999 de l'Hôpital pour enfants de Winnipeg. 1, record 22, French, - Clinique%20d%27h%C3%A9mophilie
Record 22, Spanish
Record 22, Textual support, Spanish
Record 23 - internal organization data 1999-02-05
Record 23, English
Record 23, Subject field(s)
- Genetics
Record 23, Main entry term, English
- genetic surgery
1, record 23, English, genetic%20surgery
correct
Record 23, Abbreviations, English
Record 23, Synonyms, English
Record 23, Textual support, English
Record number: 23, Textual support number: 1 DEF
Of all the therapies that pharmacologists see on the horizon, perhaps the most tantalizing are ones that would cure disease by fixing damaged genes. Diseases such as cystic fibrosis, hemophilia, and severe combined immunodeficiency are termed "single-gene" disorders because a single abnormal gene makes an abnormal protein, which, in turn, results in the sumptoms of the disease. In theory, "genetic surgery" could cure these single-gene diseases by cutting out the abnormal gene and replacing it with a working one. One might even imagine diseases with more complicated genetic underpinnings, such as certain forms of heart disease, being conquered with more extensive "genetic surgery". 1, record 23, English, - genetic%20surgery
Record 23, French
Record 23, Domaine(s)
- Génétique
Record 23, Main entry term, French
- chirurgie génétique
1, record 23, French, chirurgie%20g%C3%A9n%C3%A9tique
correct, feminine noun
Record 23, Abbreviations, French
Record 23, Synonyms, French
Record 23, Textual support, French
Record number: 23, Textual support number: 1 CONT
Enfin une intégration ciblée peut survenir. Depuis le 1er avril 1997, un programme de recherche pour le développement des techniques permettant la production en masse de sang artificiel a é mis sur pied [...] Dans un premier temps, trois groupes de chercheurs de médecins japonais étudieront les techniques actuellement disponibles pour la fabrication de plaquettes, d'hématies et de globulines. Ceci peut procéder d'une recombinaison homologue entre la séquence de transfert (donneuse) après appariement avec la séquence homologue endogène. Il s'agit d'une véritable chirurgie génétique où la régulation de l'expression génique reste naturelle. En outre, l'intégration ciblée d'une séquence réparatrice ne s'accompagne d'aucun risque de mutagénèse insertionnelle. 1, record 23, French, - chirurgie%20g%C3%A9n%C3%A9tique
Record 23, Spanish
Record 23, Textual support, Spanish
Record 24 - internal organization data 1993-10-23
Record 24, English
Record 24, Subject field(s)
- Titles of Documents and Works
Record 24, Main entry term, English
- Hemophilia, HIV & Safer Sex-The Choice is Here
1, record 24, English, Hemophilia%2C%20HIV%20%26%20Safer%20Sex%2DThe%20Choice%20is%20Here
correct, Canada
Record 24, Abbreviations, English
Record 24, Synonyms, English
Record 24, Textual support, English
Record number: 24, Textual support number: 1 OBS
National Hemophilia Foundation and Health and Welfare Canada 2, record 24, English, - Hemophilia%2C%20HIV%20%26%20Safer%20Sex%2DThe%20Choice%20is%20Here
Record 24, French
Record 24, Domaine(s)
- Titres de documents et d'œuvres
Record 24, Main entry term, French
- Hémophilie, VIH et activité sexuelle à risques réduits - à vous de décider
1, record 24, French, H%C3%A9mophilie%2C%20VIH%20et%20activit%C3%A9%20sexuelle%20%C3%A0%20risques%20r%C3%A9duits%20%2D%20%C3%A0%20vous%20de%20d%C3%A9cider
correct, Canada
Record 24, Abbreviations, French
Record 24, Synonyms, French
Record 24, Textual support, French
Record 24, Spanish
Record 24, Textual support, Spanish
Record 25 - internal organization data 1993-05-25
Record 25, English
Record 25, Subject field(s)
- International Bodies and Committees
Record 25, Main entry term, English
- World Hemophilia AIDS Center
1, record 25, English, World%20Hemophilia%20AIDS%20Center
correct
Record 25, Abbreviations, English
- WHAC 2, record 25, English, WHAC
correct, international
Record 25, Synonyms, English
Record 25, French
Record 25, Domaine(s)
- Organismes et comités internationaux
Record 25, Main entry term, French
- World Hemophilia AIDS Center
1, record 25, French, World%20Hemophilia%20AIDS%20Center
correct
Record 25, Abbreviations, French
- WHAC 2, record 25, French, WHAC
correct, international
Record 25, Synonyms, French
Record 25, Textual support, French
Record 25, Spanish
Record 25, Textual support, Spanish
Record 26 - internal organization data 1992-09-16
Record 26, English
Record 26, Subject field(s)
- Radiography (Medicine)
- Musculoskeletal System
Record 26, Main entry term, English
- tibiotalar slant
1, record 26, English, tibiotalar%20slant
correct
Record 26, Abbreviations, English
Record 26, Synonyms, English
Record 26, Textual support, English
Record number: 26, Textual support number: 1 DEF
An angled deformity of the tibiotalar joint due to asymmetrical growth of the distal tibial epiphysis. The medial aspect of the joint may be a half inch lower than the lateral articulating margin. Seen in hemophilia, juvenile rheumatoid arthritis, sickle-cell anemia, fracture, and multiple epiphyseal dysplasia. [From GBONE, 1980, p. 91 and EBONE, 1981, pp. 591, 601. ] 2, record 26, English, - tibiotalar%20slant
Record number: 26, Textual support number: 1 OBS
The tibiotalar slant may be a positioning artifact, caused by external rotation and elevation of the proximal tibia, if the central ray of the x-ray beam is not perpendicular. 3, record 26, English, - tibiotalar%20slant
Record 26, French
Record 26, Domaine(s)
- Radiographie (Médecine)
- Appareil locomoteur (Médecine)
Record 26, Main entry term, French
- bascule de l'articulation tibio-tarsienne
1, record 26, French, bascule%20de%20l%27articulation%20tibio%2Dtarsienne
correct, feminine noun
Record 26, Abbreviations, French
Record 26, Synonyms, French
Record 26, Textual support, French
Record number: 26, Textual support number: 1 DEF
Déformation en pente de l'articulation tibio-tarsienne liée à la croissance anormale de l'épiphyse tibiale. La surface interne de l'articulation se trouve plus basse que la surface articulaire externe. Les causes les plus fréquentes : hémophilie, arthrite chronique juvénile, drépanocytose, fracture et dysplasie polyépiphysaire. 2, record 26, French, - bascule%20de%20l%27articulation%20tibio%2Dtarsienne
Record number: 26, Textual support number: 1 OBS
À ne pas confondre avec un artefact résultant de la rotation externe et de l'élévation de la partie supérieure du tibia lorsque le rayon directeur n'est pas perpendiculaire au plan articulaire. 2, record 26, French, - bascule%20de%20l%27articulation%20tibio%2Dtarsienne
Record number: 26, Textual support number: 2 OBS
source d : EMSQU, 1990, A10, 31191, p. 3. 2, record 26, French, - bascule%20de%20l%27articulation%20tibio%2Dtarsienne
Record 26, Spanish
Record 26, Textual support, Spanish
Record 27 - internal organization data 1985-06-18
Record 27, English
Record 27, Subject field(s)
- Organizations, Administrative Units and Committees
Record 27, Main entry term, English
- Hemophilia Society 1, record 27, English, Hemophilia%20Society
Record 27, Abbreviations, English
Record 27, Synonyms, English
Record 27, French
Record 27, Domaine(s)
- Organismes, unités administratives et comités
Record 27, Main entry term, French
- Société de l'hémophilie 1, record 27, French, Soci%C3%A9t%C3%A9%20de%20l%27h%C3%A9mophilie
Record 27, Abbreviations, French
Record 27, Synonyms, French
Record 27, Textual support, French
Record 27, Spanish
Record 27, Textual support, Spanish
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