TERMIUM Plus®
The Government of Canada’s terminology and linguistic data bank.
RAPIDLY PROGRESSIVE DEMENTIA [2 records]
Record 1 - internal organization data 2023-07-10
Record 1, English
Record 1, Subject field(s)
- Mental Disorders
- Nervous System
Record 1, Main entry term, English
- rapidly progressive dementia
1, record 1, English, rapidly%20progressive%20dementia
correct, see observation
Record 1, Abbreviations, English
- RPD 1, record 1, English, RPD
correct
Record 1, Synonyms, English
Record 1, Textual support, English
Record number: 1, Textual support number: 1 CONT
Dementia is a clinical syndrome defined as a cognitive or behavioral decline that leads to an inability to complete daily tasks independently. Rapidly progressive dementias(RPDs) often develop over weeks to months. Although many RPDs are neurodegenerative in etiology, autoimmune, toxic/metabolic, infectious, neoplastic, and vascular processes can cause similar symptoms. As many of these latter processes are treatable, early and accurate diagnosis is important. 2, record 1, English, - rapidly%20progressive%20dementia
Record number: 1, Textual support number: 1 OBS
rapidly progressive dementia : The word "dementia" is sometimes considered pejorative. However, there is no generally accepted synonym to replace the designation "rapidly progressive dementia. " 3, record 1, English, - rapidly%20progressive%20dementia
Record 1, French
Record 1, Domaine(s)
- Troubles mentaux
- Système nerveux
Record 1, Main entry term, French
- démence à progression rapide
1, record 1, French, d%C3%A9mence%20%C3%A0%20progression%20rapide
correct, see observation, feminine noun
Record 1, Abbreviations, French
Record 1, Synonyms, French
Record 1, Textual support, French
Record number: 1, Textual support number: 1 OBS
démence à progression rapide : Le mot «démence» est parfois considéré comme péjoratif. Toutefois, il n'existe pas de synonyme généralement accepté pour remplacer la désignation «démence à progression rapide». 2, record 1, French, - d%C3%A9mence%20%C3%A0%20progression%20rapide
Record 1, Spanish
Record 1, Textual support, Spanish
Record 2 - internal organization data 2011-05-09
Record 2, English
Record 2, Subject field(s)
- Epidemiology
Record 2, Main entry term, English
- sporadic Creutzfeldt-Jakob disease
1, record 2, English, sporadic%20Creutzfeldt%2DJakob%20disease
correct
Record 2, Abbreviations, English
- sporadic CJD 2, record 2, English, sporadic%20CJD
correct
Record 2, Synonyms, English
- classical sporadic Creutzfeldt-Jakob disease 1, record 2, English, classical%20sporadic%20Creutzfeldt%2DJakob%20disease
correct
- classical sporadic CJD 1, record 2, English, classical%20sporadic%20CJD
correct
- classical sporadic CJD 1, record 2, English, classical%20sporadic%20CJD
- classical Creutzfeldt-Jakob disease 1, record 2, English, classical%20Creutzfeldt%2DJakob%20disease
correct
- classical CJD 1, record 2, English, classical%20CJD
correct
- classical CJD 1, record 2, English, classical%20CJD
Record 2, Textual support, English
Record number: 2, Textual support number: 1 DEF
A subtype of Creutzfeldt-Jakob clinically characterized by a rapidly progressive dementia, behavioural changes with progression to neurological abnormalities and onset of a progressive cerebellar syndrome, and anatomically by microvacuolar spongiform changes in the cerebellar molecular layer accompanied by reactive gliosis and neuronal loss. 1, record 2, English, - sporadic%20Creutzfeldt%2DJakob%20disease
Record number: 2, Textual support number: 1 OBS
It arises spontaneously in individuals aged between 50 and 75 without any apparent cause. 1, record 2, English, - sporadic%20Creutzfeldt%2DJakob%20disease
Record 2, French
Record 2, Domaine(s)
- Épidémiologie
Record 2, Main entry term, French
- maladie de Creutzfeldt-Jakob sporadique 1, record 2, French, maladie%20de%20Creutzfeldt%2DJakob%20sporadique
Record 2, Abbreviations, French
- MCJ sporadique 2, record 2, French, MCJ%20sporadique
correct, feminine noun
Record 2, Synonyms, French
- maladie de Creutzfeldt-Jakob sporadique classique 1, record 2, French, maladie%20de%20Creutzfeldt%2DJakob%20sporadique%20classique
correct, feminine noun
- MCJ sporadique classique 1, record 2, French, MCJ%20sporadique%20classique
correct, feminine noun
- MCJ sporadique classique 1, record 2, French, MCJ%20sporadique%20classique
- maladie de Creutzfeldt-Jakob classique 1, record 2, French, maladie%20de%20Creutzfeldt%2DJakob%20classique
correct, feminine noun
- MCJ classique 1, record 2, French, MCJ%20classique
correct, feminine noun
- MCJ classique 1, record 2, French, MCJ%20classique
Record 2, Textual support, French
Record number: 2, Textual support number: 1 DEF
Forme de la maladie de Creutzfeldt-Jakob caractérisée cliniquement par une détérioration mentale progressive, des troubles comportementaux neurologiques avec une nette prédominance cérébelleuse et, anatomiquement, par une microspongiose au niveau de la couche cellulaire, une réaction gliale avec astrocytose ainsi qu'une déperdition neuronale. 1, record 2, French, - maladie%20de%20Creutzfeldt%2DJakob%20sporadique
Record number: 2, Textual support number: 1 OBS
La cause de cette maladie, qui se déclare en moyenne vers l'âge de 60 ans et atteint les individus isolément, n'a pas encore été trouvée. 1, record 2, French, - maladie%20de%20Creutzfeldt%2DJakob%20sporadique
Record 2, Spanish
Record 2, Textual support, Spanish
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