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ANEMIE PERNICIEUSE [3 records]
Record 1 - internal organization data 2019-01-16
Record 1, English
Record 1, Subject field(s)
- Human Diseases - Various
- Blood
Universal entry(ies) Record 1
Record 1, Main entry term, English
- pernicious anemia
1, record 1, English, pernicious%20anemia
correct
Record 1, Abbreviations, English
Record 1, Synonyms, English
- Addison's anemia 2, record 1, English, Addison%27s%20anemia
correct
- Biermer's anemia 2, record 1, English, Biermer%27s%20anemia
correct
- Biermer's disease 2, record 1, English, Biermer%27s%20disease
correct
- vitamin B12 deficiency anemia due to intrinsic factor deficiency 3, record 1, English, vitamin%20B12%20deficiency%20anemia%20due%20to%20intrinsic%20factor%20deficiency
correct
- vitamin B12 deficiency anaemia due to intrinsic factor deficiency 4, record 1, English, vitamin%20B12%20deficiency%20anaemia%20due%20to%20intrinsic%20factor%20deficiency
correct, Great Britain
- addisonian anemia 2, record 1, English, addisonian%20anemia
Record 1, Textual support, English
Record number: 1, Textual support number: 1 DEF
A ... megaloblastic anemia usually seen in older adults, caused by impaired intestinal absorption of vitamin B12 due to [a defective production of] intrinsic factor [by the gastric mucosa]. 5, record 1, English, - pernicious%20anemia
Record number: 1, Textual support number: 1 OBS
D51.0: code used in the International Statistical Classification of Diseases and Related Health Problems. 6, record 1, English, - pernicious%20anemia
Record 1, Key term(s)
- pernicious anaemia
- Addison's anaemia
- addisonian anaemia
- Biermer's anaemia
- vitamin B-12 deficiency anemia due to intrinsic factor deficiency
- vitamin B-12 deficiency anaemia due to intrinsic factor deficiency
Record 1, French
Record 1, Domaine(s)
- Maladies humaines diverses
- Sang
Entrée(s) universelle(s) Record 1
Record 1, Main entry term, French
- anémie de Biermer
1, record 1, French, an%C3%A9mie%20de%20Biermer
correct, feminine noun
Record 1, Abbreviations, French
Record 1, Synonyms, French
- anémie pernicieuse 2, record 1, French, an%C3%A9mie%20pernicieuse
correct, feminine noun
- maladie de Biermer 3, record 1, French, maladie%20de%20Biermer
correct, feminine noun
- anémie par carence en vitamine B12 due à une carence en facteur intrinsèque 4, record 1, French, an%C3%A9mie%20par%20carence%20en%20vitamine%20B12%20due%20%C3%A0%20une%20carence%20en%20facteur%20intrins%C3%A8que
correct, feminine noun
- anémie d’Addison 5, record 1, French, an%C3%A9mie%20d%26rsquo%3BAddison
feminine noun
Record 1, Textual support, French
Record number: 1, Textual support number: 1 DEF
Anémie sidéroblastique macrocytaire par carence en vitamine B12 due à un tarissement de la sécrétion du facteur intrinsèque par l’estomac empêchant l’absorption de la vitamine B12. 6, record 1, French, - an%C3%A9mie%20de%20Biermer
Record number: 1, Textual support number: 1 OBS
D51.0 : code de la Classification statistique internationale des maladies et des problèmes de santé connexes 7, record 1, French, - an%C3%A9mie%20de%20Biermer
Record 1, Key term(s)
- anémie par carence en vitamine B-12 due à une carence en facteur intrinsèque
Record 1, Spanish
Record 1, Campo(s) temático(s)
- Enfermedades humanas varias
- Sangre
Entrada(s) universal(es) Record 1
Record 1, Main entry term, Spanish
- anemia perniciosa
1, record 1, Spanish, anemia%20perniciosa
correct, feminine noun
Record 1, Abbreviations, Spanish
Record 1, Synonyms, Spanish
Record 1, Textual support, Spanish
Record number: 1, Textual support number: 1 DEF
Enfermedad derivada de la carencia de una sustancia esencial para la absorción de vitamina B12 y la maduración de hematíes y otras células sanguíneas, en la que una reducción del número de células sanguíneas afecta a los sistemas gastrointestinal y neurológico. 2, record 1, Spanish, - anemia%20perniciosa
Record 2 - internal organization data 2003-05-09
Record 2, English
Record 2, Subject field(s)
- Immunology
- Biotechnology
Record 2, Main entry term, English
- intrinsic factor
1, record 2, English, intrinsic%20factor
correct
Record 2, Abbreviations, English
Record 2, Synonyms, English
Record 2, Textual support, English
Record number: 2, Textual support number: 1 DEF
A glycoprotein secreted by the parietal cells of the gastric glands, necessary for the absorption of vitamin B12 (cyanocobalamin, extrinsic factor). Lack of intrinsic factor, with consequent deficiency in vitamin B12, results in pernicious anemia. 2, record 2, English, - intrinsic%20factor
Record 2, French
Record 2, Domaine(s)
- Immunologie
- Biotechnologie
Record 2, Main entry term, French
- facteur intrinsèque
1, record 2, French, facteur%20intrins%C3%A8que
correct, masculine noun
Record 2, Abbreviations, French
Record 2, Synonyms, French
Record 2, Textual support, French
Record number: 2, Textual support number: 1 DEF
Glycoprotéine sécrétée par les cellules pariétales de l'estomac et dont la fonction est de lier la vitamine B12 et ainsi de permettre son absorption intestinale. Les anticorps antifacteur intrinsèque préviennent la fixation de la vitamine B12 sur le facteur intrinsèque en recouvrant le site de liaison. [...] Les anticorps antifacteur intrinsèque sont présents dans près de 60 à 70 p. 100 des cas(d’anémie pernicieuse) dans le sérum ou dans le liquide gastrique. 2, record 2, French, - facteur%20intrins%C3%A8que
Record 2, Spanish
Record 2, Campo(s) temático(s)
- Inmunología
- Biotecnología
Record 2, Main entry term, Spanish
- factor intrínseco
1, record 2, Spanish, factor%20intr%C3%ADnseco
correct, masculine noun
Record 2, Abbreviations, Spanish
Record 2, Synonyms, Spanish
Record 2, Textual support, Spanish
Record 3 - internal organization data 1986-08-13
Record 3, English
Record 3, Subject field(s)
- Genetics
Record 3, Main entry term, English
- spontaneous chromosomal breakage
1, record 3, English, spontaneous%20chromosomal%20breakage
correct
Record 3, Abbreviations, English
Record 3, Synonyms, English
Record 3, Textual support, English
Record number: 3, Textual support number: 1 DEF
Phenomenon producing either a loss of chromosomal material or a structural modification without any change in the quantity of material and produced by a cause which is not known. 1, record 3, English, - spontaneous%20chromosomal%20breakage
Record number: 3, Textual support number: 1 CONT
Spontaneous chromosomal breakage has been found in six inherited diseases: ataxia telangiectasia, glutathione reductase deficiency, Kostmann's agranulocytosis and pernicious anemia. 1, record 3, English, - spontaneous%20chromosomal%20breakage
Record 3, French
Record 3, Domaine(s)
- Génétique
Record 3, Main entry term, French
- cassure chromosomique spontanée
1, record 3, French, cassure%20chromosomique%20spontan%C3%A9e
correct, feminine noun
Record 3, Abbreviations, French
Record 3, Synonyms, French
Record 3, Textual support, French
Record number: 3, Textual support number: 1 DEF
Phénomène provoquant soit une perte de matériel chromosomique, soit une modification de structure sans que la quantité de matériel soit changée, et se déclenchant sans cause décelable. 1, record 3, French, - cassure%20chromosomique%20spontan%C3%A9e
Record number: 3, Textual support number: 1 CONT
(Le syndrome de Bloom) Les anomalies chromosomiques font rentrer ces deux observations dans le cadre des "cassures chromosomiques spontanées" englobant, selon Schroeder et Kurt(1971), six maladies héréditaires : le syndrome de Bloom, l'anémie de Fanconi, l'ataxie télangiectasie, le déficit en glutathion peroxydase, l'agranulocytose de Kostmann et l'anémie pernicieuse. 1, record 3, French, - cassure%20chromosomique%20spontan%C3%A9e
Record 3, Spanish
Record 3, Textual support, Spanish
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