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Record 1,  Textual support,  English

Record number: 1, Textual support number: 1 CONT

Central areolar choroidal dystrophy (CACD) is a hereditary retinal disorder that primarily affects the macula. In the early stages, there is subtle, mottled depigmentation in the posterior pole. Ultimately, the depigmentation enlarges into in a well-circumscribed round or oval area of atrophy of the retinal pigment epithelium (RPE) and choriocapillaris in the center of the macula. Patients usually become symptomatic in the [third] to [fourth] decade when a fine, hardly detectable, mottling of the RPE leads to the development of absolute central visual scotomas. Later, between the [fourth] and [seventh] decade of life, progressive macular atrophy leads to a dramatic decline in central visual acuity and severe visual disability. CACD may be autosomal dominant or recessive; however, autosomal-recessive cases are rare. Although CACD has a genetic basis, sporadic cases have been reported.  3, record 1, English, - central%20areolar%20choroidal%20dystrophy

Record 1,  Textual support,  French

Record number: 1, Textual support number: 1 DEF

Atrophie aréolaire centrale maculaire héréditaire et primitive aux bords nets avec quelques petites taches jaunâtres ressemblant à des druses autour de la lésion ou au pôle postérieur.  1, record 1, French, - dystrophie%20choro%C3%AFdienne%20ar%C3%A9olaire%20centrale

Record 1,  Textual support,  Spanish