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Record 1,  Textual support,  English

Record number: 1, Textual support number: 1 CONT

Retinal pattern dystrophies are a slowly progressive heterogeneous group of primarily autosomal dominantly inherited macular diseases whose unifying element involves the deposition of pigment in the retinal pigment epithelium (RPE) of the macula. Although findings are classically and most often centered in the macula, pigment deposition may also occur in the periphery. Depending on the distribution pattern, these pattern dystrophies can be separated into major categories or types. These include reticular dystrophy, fundus pulverulentus, butterfly-shaped pigment dystrophy, adult-onset foveomacular vitelliform dystrophy, and multifocal pattern dystrophy simulating Stargardt disease.  2, record 1, English, - pattern%20dystrophy

Record 1,  Textual support,  French

Record number: 1, Textual support number: 1 CONT

Les dystrophies réticulées regroupent de nombreux phénotypes, incluant entre autres la dystrophie pseudo-vitelliforme de l'adulte, les dystrophies réticulées en ailes de papillon, les dystrophies réticulées de l'EP [épithélium pigmentaire], les pseudo-Stargardt, les fundus pulveruluntus.  1, record 1, French, - dystrophie%20r%C3%A9ticul%C3%A9e

Record 1,  Textual support,  Spanish

Record 2,  Textual support,  English

Record number: 2, Textual support number: 1 CONT

Adult-onset vitelliform macular dystrophy (AVMD) is an inherited maculopathy characterized by metamorphopsias and decrease in visual acuity occurring between the fourth and the sixth decade. It is characterized by an "egg yolk" macular lesion eventually evolving towards foveal atrophy and fibrosis.  8, record 2, English, - adult%2Donset%20vitelliform%20macular%20dystrophy

Record number: 2, Textual support number: 2 CONT

Adult vitelliform macular dystrophy. ... It is characterized by a focal, round or oval shaped, subretinal yellowish foveal lesion, often with one or more pigment stops on the anterior surface at the level of the pigment epithelium. The lesions may vary in size but are typically one third to one half of a disc diameter, and are usually bilateral and symmetrical. Patients usually present in the fourth or fifth decade of life and tend to have minimal visual symptoms ... The disorder differs from ... Best's disease ... in that foveal lesions are smaller, it presents at a later age, it does not demonstrate evolutionary changes of the foveal lesion, and the light-induced rise in ocular potential is rarely absent.  9, record 2, English, - adult%2Donset%20vitelliform%20macular%20dystrophy

Record 2,  Textual support,  French

Record number: 2, Textual support number: 1 CONT

Dystrophie pseudo-vitelliforme de l'adulte. [...] Elle est caractérisée par un dépôt de matériel souvent unique et arrondi, à l'aspect de «jaune d’œuf sur le plat», similaire à l'aspect précoce de la dystrophie vitelliforme de Best, avec laquelle elle a souvent été confondue. Son évolution tend vers l'atrophie maculaire ou plus rarement, vers la néovascularisation.  3, record 2, French, - dystrophie%20maculaire%20vitelliforme%20de%20l%26rsquo%3Badulte

Record 2,  Textual support,  Spanish