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MALADIE CHAINES LOURDES [4 records]
Record 1 - internal organization data 2011-05-16
Record 1, English
Record 1, Subject field(s)
- Blood
- Immunology
Record 1, Main entry term, English
- mu chain disease
1, record 1, English, mu%20chain%20disease
correct
Record 1, Abbreviations, English
Record 1, Synonyms, English
- mu heavy chain disease 2, record 1, English, mu%20heavy%20chain%20disease
correct
Record 1, Textual support, English
Record number: 1, Textual support number: 1 DEF
The rarest heavy chain disease, found in patients with chronic lymphocytic leukemia, with symptoms of hepatomegaly and splenomegaly. 1, record 1, English, - mu%20chain%20disease
Record 1, French
Record 1, Domaine(s)
- Sang
- Immunologie
Record 1, Main entry term, French
- maladie des chaînes lourdes mu
1, record 1, French, maladie%20des%20cha%C3%AEnes%20lourdes%20mu
correct, feminine noun
Record 1, Abbreviations, French
Record 1, Synonyms, French
Record 1, Textual support, French
Record number: 1, Textual support number: 1 DEF
Variété de maladie des chaînes lourdes s'associant, dans la moitié des cas, à une leucémie lymphoïde chronique ou se présentant sous la forme d'autres syndromes immunoprolifératifs. 2, record 1, French, - maladie%20des%20cha%C3%AEnes%20lourdes%20mu
Record 1, Spanish
Record 1, Textual support, Spanish
Record 2 - internal organization data 2004-02-27
Record 2, English
Record 2, Subject field(s)
- Cancers and Oncology
- Cytology
Record 2, Main entry term, English
- heavy-chain disease
1, record 2, English, heavy%2Dchain%20disease
correct
Record 2, Abbreviations, English
Record 2, Synonyms, English
Record 2, Textual support, English
Record number: 2, Textual support number: 1 DEF
A group of rare malignant neoplasms of lymphoplasmacytic cells that secrete an M component consisting of monoclonal immunoglobulin heavy chains or heavy chain fragments; they are classified according to heavy chain type. 1, record 2, English, - heavy%2Dchain%20disease
Record 2, Key term(s)
- heavy chain disease
Record 2, French
Record 2, Domaine(s)
- Cancers et oncologie
- Cytologie
Record 2, Main entry term, French
- maladie des chaînes lourdes
1, record 2, French, maladie%20des%20cha%C3%AEnes%20lourdes
correct, feminine noun
Record 2, Abbreviations, French
- MCL 2, record 2, French, MCL
correct, feminine noun
Record 2, Synonyms, French
Record 2, Textual support, French
Record number: 2, Textual support number: 1 DEF
Entité qui englobe trois gammapathies monoclonales caractérisées par l'élaboration excessive d'une partie des chaînes lourdes d'une immunoglobine spécifique, comprenant habituellement le fragment Fc. 1, record 2, French, - maladie%20des%20cha%C3%AEnes%20lourdes
Record 2, Spanish
Record 2, Campo(s) temático(s)
- Tipos de cáncer y oncología
- Citología
Record 2, Main entry term, Spanish
- enfermedad de cadena pesada
1, record 2, Spanish, enfermedad%20de%20cadena%20pesada
correct, feminine noun
Record 2, Abbreviations, Spanish
Record 2, Synonyms, Spanish
Record 2, Textual support, Spanish
Record number: 2, Textual support number: 1 DEF
Alteraciones linfoplasmacíticas poco frecuentes y caracterizadas por la proliferación de células secretoras de una porción de la molécula de inmunoglobulina. 1, record 2, Spanish, - enfermedad%20de%20cadena%20pesada
Record 3 - internal organization data 2002-07-30
Record 3, English
Record 3, Subject field(s)
- Endocrine System and Metabolism
- Lymphatic System
Record 3, Main entry term, English
- gamma-heavy-chain disease
1, record 3, English, gamma%2Dheavy%2Dchain%20disease
correct
Record 3, Abbreviations, English
- gamma-HCD 1, record 3, English, gamma%2DHCD
correct
Record 3, Synonyms, English
- Franklin disease 1, record 3, English, Franklin%20disease
correct
Record 3, Textual support, English
Record number: 3, Textual support number: 1 CONT
The heavy-chain diseases (HCDs) are lymphoplasmacytic proliferative disorders characterized by the uncontrolled production of abnormal, often structurally incomplete, immunoglobulin heavy chains. ... The most often studied HCD is gamma-HCD, or Franklin disease ... 1, record 3, English, - gamma%2Dheavy%2Dchain%20disease
Record 3, Key term(s)
- gamma heavy chain disease
- gamma HCD
Record 3, French
Record 3, Domaine(s)
- Systèmes endocrinien et métabolique
- Système lymphatique
Record 3, Main entry term, French
- maladie des chaînes lourdes gamma
1, record 3, French, maladie%20des%20cha%C3%AEnes%20lourdes%20gamma
correct, feminine noun
Record 3, Abbreviations, French
Record 3, Synonyms, French
- maladie de Franklin 1, record 3, French, maladie%20de%20Franklin
correct, feminine noun
Record 3, Textual support, French
Record number: 3, Textual support number: 1 DEF
Maladie des chaînes lourdes caractérisée par une prolifération lymphoplasmocytaire polymorphe, ganglionnaire, hépatosplénique et médullaire avec parfois érythème palatin et oedème de la luette. 1, record 3, French, - maladie%20des%20cha%C3%AEnes%20lourdes%20gamma
Record 3, Spanish
Record 3, Textual support, Spanish
Record 4 - internal organization data 1998-06-01
Record 4, English
Record 4, Subject field(s)
- Histology
Record 4, Main entry term, English
- alpha chain disease
1, record 4, English, alpha%20chain%20disease
correct
Record 4, Abbreviations, English
Record 4, Synonyms, English
- alpha heavy chain disease 2, record 4, English, alpha%20heavy%20chain%20disease
correct
Record 4, Textual support, English
Record number: 4, Textual support number: 1 DEF
The most common heavy chain disease, occurring predominantly in young adults in the Mediterranean area, and characterized by plasma cell infiltration of the lamina propria of the small intestine resulting in malabsorption, with diarrhea, abdominal pain, and weight loss, or, exceedingly rarely, by pulmonary involvement. 1, record 4, English, - alpha%20chain%20disease
Record 4, French
Record 4, Domaine(s)
- Histologie
Record 4, Main entry term, French
- maladie des chaînes alpha
1, record 4, French, maladie%20des%20cha%C3%AEnes%20alpha
correct, feminine noun
Record 4, Abbreviations, French
Record 4, Synonyms, French
- maladie des chaînes lourdes alpha 1, record 4, French, maladie%20des%20cha%C3%AEnes%20lourdes%20%20alpha
correct, feminine noun
Record 4, Textual support, French
Record number: 4, Textual support number: 1 DEF
La variété la plus fréquente de maladie des chaînes lourdes, elle affecte le système de l'IgA sécrétoire. La forme digestive est la plus fréquente, avec prolifération lymphoplasmocytaire infiltrant la totalité de l'intestin grêle et les ganglions mésentériques, avec une atrophie villositaire et un syndrôme de malabsorption intestinale grave. 1, record 4, French, - maladie%20des%20cha%C3%AEnes%20alpha
Record 4, Spanish
Record 4, Textual support, Spanish
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